Bony cochlear nerve canal and internal auditory canal measures predict cochlear nerve status
Objectives The bony cochlear nerve canal is the space between the fundus of the internal auditory canal and the base of the cochlear modiolus that carries cochlear nerve fibres. This study aimed to determine the distribution of bony labyrinth anomalies and cochlear nerve anomalies in patients with bony cochlear nerve canal and internal auditory canal […]
Novel pathogenic variants underlie SLC26A4 -related hearing loss in a multiethnic cohort
Objectives: The genetics of sensorineural hearing loss is characterized by a high degree of heterogeneity. Despite this heterogeneity, DNA variants found within SLC26A4 have been reported to be the second most common contributor after those of GJB2 in many populations. Methods: Whole exome sequencing and/or Sanger sequencing of SLC26A4 in 117 individuals with sensorineural hearing […]
Classification and Current Management of Inner Ear Malformations
Morphologically congenital sensorineural hearing loss can be investigated under two categories. Majority of the congenital hearing loss (80%) are membranous malformations. Here the pathology involves inner ear hair cells. There is no gross bony abnormality and therefore, in these cases, high resolution computerized tomography and MRI of the temporal bone reveal normal findings. Remaining 20% […]
RAMSAY-HUNT SYNDROME WITH MULTINEUROPATHY
Ramsay-Hunt Syndrome (RHS) is an infectious cranial neuropathy due to reactivation of varicella zoster virus in the geniculate ganglion. In this case report, we present 2 cases of RHS with unilateral facial palsy, herpetic vesicles on the auricle and multiple cranial nerve involvement treated with intravenous and oral corticosteroids, antiviral agents and antibiotics. Early diagnosis […]
Classification of Inner Ear Malformations
Morphologically congenital sensorineural hearing loss (SNHL) can be investigated under two categories. Majority of the congenital hearing loss (80 %) are membranous malformations. Here the pathology involves inner ear hair cells. There is no gross bony abnormality and, therefore, in these cases, high-resolution computerized tomography (HRCT) and magnetic resonance imaging (MRI) of the temporal bone […]
The effect of cochlear implant bed preparation and fixation technique on the revision cochlear implantation rate
Objective This study aimed to determine the effect of the subperiosteal tight pocket technique versus the bone recess with suture fixation technique on the revision cochlear implantation rate and complications. Methods This retrospective study included 1514 patients who underwent cochlear implantation by 2 senior surgeons between October 2002 and January 2016. Revision cases were identified […]
Traumatic Facial and Vestibulocochlear Nerve Injury in The Internal Acoustic Canal in The Absence of A Temporal Bone Fracture
We present a rare case of traumatic facial and vestibulocochlear nerve injury in the internal acoustic canal in the absence of a temporal bone fracture. A 2.5-year-old female presented with sudden-onset left-sided facial paralysis and ipsilateral total hearing loss after being hit by a falling television. High-resolution computed tomography revealed an occipital fracture line that […]
Another evidence for pressure transfer mechanism in incomplete partition two anomaly via enlarged vestibular aqueduct
A female patient with unilateral enlarged vestibular aqueduct (EVA) demonstrated scala vestibuli dilatation on that side while on the contralateral side both vestibular aqueduct and scala vestibuli were normal. This important radiological finding demonstrates that modiolar defects (hence ‘cystic apex’) observed in Incomplete partition-II is due to pressure transfer via EVA during embryological development. Therefore, […]
The Association Between Modiolar Base Anomalies and Intraoperative Cerebrospinal Fluid Leakage in Patients With Incomplete Partition Type-II Anomaly: A Classification System and Presentation of 73 Cases
Objective: Modiolus and modiolar base abnormalities in patients with incomplete partition-II anomaly (IP-II) increase the risk of intraoperative cerebrospinal fluid (CSF) leakage. This study aimed to classify modiolar abnormalities and define objective radiological measures for preoperatively evaluating intraoperative CSF leakage risk. Study Design: Retrospective case series. Setting: Tertiary referral center. Patients: The study included 73 […]
The Effect of National Pneumococcal Vaccination Program on Incidence of Postmeningitis Sensorineural Hearing Loss and Current Treatment Modalities
Objectives: The aim of the present study was to investigate the effect of the national pneumococcal vaccination program on postmeningitis sensorineural hearing loss (SNHL). Materials and methods: Overall, 2751 patients (2615 cochlear implantation and 136 auditory brainstem implantation) who underwent cochlear implantation (CI) and auditory brainstem implantation (ABI) at a tertiary referral hospital otolaryngology clinic […]
Giant sphenoid sinus. A case report
A rare case of giant sphenoid sinus with excessive pneumatization is presented. The relevant literature is discussed.
Contralateral Non-Auditory Stimulation in Auditory Brainstem Implantation: A Case Report
A 2-years-old girl was diagnosed with pontocerebellar hypoplasia and bilateral cochlear nerve aplasia. She was implanted with auditory brainstem implant (ABI) on the left ear. During the initial stimulation of the ABI, only three electrodes could be activated in follow-up visits due to the contralateral facial nerve stimulation. In case of three activated electrodes, her […]
Histopathology of Inner Ear Malformations: Potential Pitfalls for Cochlear Implantation
Hypothesis: The presence of bony inner ear malformations may associate with a number of anatomical abnormalities affecting the middle ear structures. Those malformations may create pitfalls and complications for cochlear implantation. Background: Inner ear malformations associate with varying degrees of hearing loss, and frequently require cochlear implantation for hearing rehabilitation. Therefore, the abnormalities affecting the […]
Cochlear Nerve Hypoplasia: Audiological Characteristics in Children and Adults
Background: Cochlear nerve deficiency is a general term used to describe both cochlear nerve hypoplasia (CNH) and cochlear nerve aplasia. Although these two conditions can have similar results on audiological evaluation, CNH yields more variation in audiological tests. Objectives: To describe the audiological characteristics of the CNH cases in our series in relation to radiological […]
A study on modelling cochlear duct mid-scalar length based on high-resolution computed tomography, and its effect on peri-modiolar and mid-scalar implant selection
Objective To determine cochlear duct mid-scalar length in normal cochleae and its role in selecting the correct peri-modiolar and mid-scalar implant length. Methods The study included 40 patients with chronic otitis media who underwent high-resolution computed tomography of the temporal bone. The length and height of the basal turn, mid-modiolar height of the cochlea, mid-scalar […]
Evaluation of the Postural Stability and Sensory Integration Disorders in Pediatric Cochlear Implant Users with Inner Ear Malformations
Purpose: The aim of this study was to evaluate and compare the postural stability and sensory integration disorders of pediatric cochlear implant users with and without inner ear malformations. Material and Methods: The control group consists of 20 cochlear implant users with normal cochlea whereas the study group comprises 20 cochlear implant users with inner […]
Wideband tympanometry findings in inner ear malformations
Objective: The deficits in the cochlea which is at the one end of the ear sound transfer system, may effect middle ear functions. Wideband typanometry (WBT) is frequently used to evaluate these transfer functions which play a crucial role in setting the impedance matching between the external ear and the cochlea. To this end, the […]